暂无数据
产品名称
起订量
单价(含增值税)
库存(PCS)
起订数量
产品简介
英文名称 | Anti-GLA Polyclonal Antibody |
靶标 | GLA |
别名 | GALA;Alpha-galactosidase A;Alpha-D-galactosidase A;Alpha-D-galactoside galactohydrolase;Galactosylgalactosylglucosylceramidase GLA;Melibiase; Agalsidase;AGAL_HUMAN;Agalsidase alfa;Alpha D galactosidase A;Alpha gal A; |
宿主 | Rabbit |
稀释比例 | IHC 1:50-200. |
Gene ID | 2717 |
保存 | Store at -20°C. Avoid freeze / thaw cycles. |
Swiss Prot | P06280 |
蛋白分子量 | 79kDa |
储存液 | Buffer: PBS with 0.03% Proclin300, 50% glycerol, pH7.3. |
亚细胞定位 | Cytoplasm |
免疫原 | Recombinant protein of human GLA |
亚型 | IgG |
纯化方法 | Affinity purification |
背景资料 | This gene encodes a homodimeric glycoprotein that hydrolyses the terminal alpha-galactosyl moieties from glycolipids and glycoproteins. This enzyme predominantly hydrolyzes ceramide trihexoside, and it can catalyze the hydrolysis of melibiose into galactose and glucose. A variety of mutations in this gene affect the synthesis, processing, and stability of this enzyme, which causes Fabry disease, a rare lysosomal storage disorder that results from a failure to catabolize alpha-D-galactosyl glycolipid moieties. |
Public Immunogen Range | 1-350aa |
克隆类型 | Polyclonal Antibody |
交叉反应 | Human;Mouse |
应用 | IHC |
规格 | 50ul100ul |
注意:
1.本产品仅供科研使用。请勿用于医药、临床诊断或治疗,食品及化妆品等用途。请勿存放于普通住宅区。
2.为了您的安全和健康,请穿好实验服并佩戴一次性手套和口罩操作。
暂无数据
我要询价
*联系方式:
(可以是QQ、MSN、电子邮箱、电话等,您的联系方式不会被公开)
*内容: